Celiac disease is an autoimmune-based digestive disease and it is an immune-mediated enteropathy due to the ingestion of a gluten containing diet. Individuals predisposed to risk are genetically predetermined. Symptoms of the disease at a large usually start at the very early part of life just after weaning, however, a small group of patient present late we called it ‘latent celiac sprue”. We present a rare case of young patient having celiac disease with symptomatic idiopathic portal hypertension.