
Carcinosarcoma of the ovary is also known as Malignant Mixed Mullerian Tumour. It is an ovarian neoplasm with an incidence of 1-3% of all ovarian neoplasms. Usually, patients are postmenopausal women with a history of low parity. We report a rare case of 44 years old woman who presented with complaints of amenorrhea and pain in the abdomen of three months duration. Per speculum and per vaginum examination showed a mass of size 10x 8 cm in the right iliac fossa. Ultrasonogram and CT scan revealed a neoplastic mass in the right adnexa. CA-125 levels were 714U/ml. The patient underwent staging laparotomy and was found to be in stage 4a. Microscopic examination showed the presence of both carcinomatous and sarcomatous components with rhabdomyosarcomatous and chondrosarcomatous differentiation. The immunohistochemistry confirmed rhabdomyosarcomatous differentiation. The final diagnosis of carcinosarcoma or ovarian malignant mixed mullerian tumour (OMMMT) was rendered.