A rare variant of caudal regression syndrome mimicking ohvira syndrome

Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA), or Herlyn-Werner-Wunderlich syndrome (HWWS), is a rare congenital mullerian and mesonephric anomalies presenting with a characteristic triad of uterine didelphys, unilateral obstructed hemivagina, and ipsilateral renal agenesis .suspicion and knowledge of this anomaly are essential for a precise diagnosis. Caudal regression syndrome (CRS) is characterized by a wide range of abnormalities including partial absence of sacrum or coccyx with no apparent associated anamolies to extensive deformity of the lower vertebrae, pelvis and fused lower limbs (sirenomelia).Herein we report a case of 16 year old girl, a case of CRS mimicking OHVIRA.