Neurenteric cysts are congenital lesions of the spinal cord which usually communicate to other endodermally derived structures of the body, the embryological theory of which is yet not properly established. They are usually located in the cervico-dorsal region of the spinal cord with an associated vertebral anomaly like spina bifida, butterfly vertebra, lack of segmentation, partial fusion, scoliosis together with the cyst. However, only few cases have been reported in literature where the cysts have not been associated with any vertebral anomalies.