Odontodysplasia is a rare nonhereditary developmental anomaly of dental hard tissue with unknown etiology, arising from both ectodermal and mesodermal components. Hitchin in 1934 first described it as a localized arrest of tooth development generally affecting one quadrant of the jaw. When it just affects one quadrant, it is referred to as “Regional Odontodysplasia,” but when it crosses the midline and affects more than one quadrant, it is referred to as “Generalised Odontodysplasia.” In this case, 10 year old female patient was diagnosed with Regional Odontodysplasia affecting the Maxillary Anterior Teeth on left side confirmed with Clinical and Radiographic Features.