Unicornuate uterus with noncommunicating functional horn: a case report

Mullerian duct anomalies represent a group of congenital anomalies that result from arrested development, or incomplete fusion of the mesonephric ducts. The incidence of congenital mullerian anomalies is 1/200 to 1/600. The incidence of rudimentary horn is very rare (1:100,000). Approximately 75% of such horns do not communicate with the normal hemiuterus. These uterine anomalies are either diagnosed incidentally or the patient may present with obstetrical or gynecological problems. Vaginal obstruction is associated with perivaginal mass, pain, and endometriosis, but cyclic menstrual flow may be present because of the normally functioning opposite side. This anomaly is usually associated with ipsilateral renal agenesis (67%) or ipsilateral pelvic kidney. Laparotomy has been the standard approach for such cases. We report this case in hope of expanding the knowledge of a rare occurrence.